X-linked agammaglobulinemia (XLA) is one of the commonest primary immune deficiencies
encountered in pediatric clinical practice. In adults, common variable immunodeficiency …

Kawasaki disease (KD) has replaced acute rheumatic fever as the most common cause of
acquired heart disease in children in the developed world and is increasingly being …

Purpose Deficiency of interleukin-1 receptor antagonist (DIRA) is a rare life-threatening
autoinflammatory disease caused by autosomal recessive mutations in IL1RN. DIRA …

3. Psaltis AJ, Weitzel EK, Ha KR, Wormald PJ. The effect of bacterial biofilms on post-sinus
surgical outcomes. Am J Rhinol 2008; 22: 1-6. 4. Prince AA, Steiger JD, Khalid AN …

Aim Kawasaki disease (KD) is a medium vessel vasculitis of childhood. In infancy KD is
often characterized by incomplete and atypical forms. There is paucity of literature on KD in …

Background Thromboembolism is a rare life-threatening complication of childhood nephrotic
syndrome. Methods We present the clinical profile and outcome of 34 children with 35 …

Objective To estimate incidence of Kawasaki disease (KD) over time among children in the
city of Chandigarh, North India. Patients and methods We analysed records of all children …

Background Chronic granulomatous disease (CGD) is an inherited defect in phagocytic
respiratory burst that results in severe and life-threatening infections in affected children …

Background Severe Combined Immune Deficiency (SCID) is an inherited defect in
lymphocyte development and function that results in life-threatening opportunistic infections …

Purpose Chronic granulomatous disease (CGD) is an inherited phagocytic disorder
characterized by recurrent infections with usually catalase-positive organisms. Infections in …