Objective Pulmonary hypertension (PH) is a frequent and life‐limiting complication of
systemic sclerosis (SSc). However, data on survival rates and their evolution over time, as …

As the diagnosis of systemic sclerosis (SSc) is generally suggested by the presence of
Raynaud's phenomenon followed by typical skin thickening associated with the presence of …

Primary Sjögren syndrome (pSS) is a fairly common autoimmune disease with glandular
and extraglandular manifestations. Pulmonary involvement mainly corresponds to small …

Importance High-dose immunosuppressive therapy and autologous hematopoietic stem cell
transplantation (HSCT) have shown efficacy in systemic sclerosis in phase 1 and small …

Objective Screening allows for early management of pulmonary arterial hypertension (PAH),
a severe complication of systemic sclerosis (SSc). Since no consensus has been reached …

Histiocytoses are rare disorders of unknown origin with highly heterogeneous prognosis.
BRAF mutations have been observed in Langerhans cell histiocytosis (LCH). We …

Objective Pulmonary arterial hypertension (PAH) is a severe, life‐limiting complication of
systemic sclerosis (SSc). Guidelines recommend early detection and management of SSc …

Objective To describe the response to first‐line immunosuppressive therapy with or without
pulmonary vasodilators in pulmonary arterial hypertension (PAH) associated with systemic …

Objectives: To assess the prevalence and patterns of cardiac abnormalities as detected by
cardiac magnetic resonance imaging (MRI) in systemic sclerosis (SSc). Methods: Fifty-two …

OBJECTIVE: To describe the natural history of ischemic digital ulcers (DU) in systemic
sclerosis (SSc). METHODS: This single-center, retrospective, longitudinal study identified …