Clinical data of patients regarding fulfilling 1990 ACR CSS classification criteria and 2017 ACR/EULAR Draft Criteria for EGPA
| 1990 ACR CCS classification criteria (4/6 for classification)14 | Case 1 | Case 2 | Draft ACR/EULAR Criteria for EGPA (>5 points for classification)15 | Case 1 (total score: 8) | Case 2 (total score: 11) |
| Asthma | Yes | Yes | Obstructive airways disease (+3) | +3 | +3 |
| Paranasal sinus abnormality | Yes | No | Nasal polyps (+3) | No | +3 |
| Mononeuropathy (including multiplex) or polyneuropathy | No | No | Mononeuritis multiplex or motor neuropathy (+1) | No | No |
| Eosinophilia >10% on differential white blood cell count | Yes | Yes | Eosinophil count >109/mL (+5) | +5 | +5 |
| Biopsy containing a blood vessel with extravascular eosinophils | Not done | Not done | Extravascular eosinophil predominant inflammation/increased eosinophils in bone marrow (2) | Not done | Not done |
| Non‐fixed pulmonary infiltrates on roentgenography | Yes | Yes | |||
| Microscopic haematuria (−1) | No | No | |||
| c-ANCA or PR3-antibody positivity (−3) | Negative | Negative |
ACR, American College of Rheumatology; c-ANCA, cytoplasmic antineutrophil cytoplasmic antibody; CSS, Churg-Strauss syndrome; EGPA, eosinophilic granulomatosis with polyangiitis; EULAR, European League Against Rheumatism.