Clinical domains and criteria | Weight (points) | Immunological domains and criteria | Weight (points) |
Constitutional | Antiphospholipid antibodies | ||
Fever | 13 | Anticardiolipin IgG >40 GPL units or anti-β2GP1 IgG >40 units or lupus anticoagulant positive | 13 |
Haematological | Complement proteins | ||
Leucopaenia | 12 | Low C3 or low C4 | 19 |
Thrombocytopaenia | 26 | Low C3 and low C4 | 27 |
Autoimmune haemolysis | 28 | SLE-specific antibodies | |
Neuropsychiatric | Anti-dsDNA antibody | 38 | |
Delirium | 12 | Anti-Smith antibody | 40 |
Psychosis | 20 | ||
Seizure | 34 | ||
Mucocutaneous | |||
Non-scarring alopecia | 13 | ||
Oral ulcers | 14 | ||
Subacute cutaneous or discoid lupus* | 29* | ||
Acute cutaneous lupus | 38 | ||
Serositis | |||
Pleural or pericardial effusion | 34 | ||
Acute pericarditis | 38 | ||
Musculoskeletal | |||
Synovitis in ≥2 joints | 34 | ||
Renal | |||
Proteinuria>0.5 g/24 hours | 27 | ||
Renal biopsy with Class II or V lupus nephritis | 55 | ||
Renal biopsy with Class III or IV lupus nephritis | 74 |
*Subacute cutaneous lupus and discoid lupus each received a weight of 29.
SLE, systemic lupus erythematosus.