Characteristics of patients with IgG4-related disease
| Clinical parameters | |
| IgG4-RD responder index, median (range) | 12 (6–21) |
| Serum IgG (mg/dl), median (range) | 1729 (934–3593) |
| Serum IgG4 (mg/dL), median (range) | 387.5 (65–2178) |
| Soluble IL-2 receptor (U/mL), median (range) | 448 (202–1963) |
| Atopic features | |
| Past atopic history, n (%) | 17 (61%) |
| Serum IgE (IU/mL), median (range) | 310 (38–3300) |
| Blood eosinophil count (cells/µL), median (range) | 231 (62–1568) |
| Organs involved | |
| Number of affected organs, median (range) | 3 (1–6) |
| Lacrimal gland and orbit, n (%) | 22 (79%) |
| Salivary gland, n (%) | 19 (68%) |
| Lymph node, n (%) | 16 (57%) |
| Lung, n (%) | 7 (25%) |
| Pancreas, n (%) | 7 (25%) |
| Kidney, n (%) | 5 (18%) |
| Retroperitoneum, n (%) | 3 (11%) |
| Aorta, n (%) | 2 (7%) |
| Skin, n (%) | 2 (7%) |
| Breast, n (%) | 1 (4%) |
| Paravertebral mass, n (%) | 1 (4%) |
IgG4-RD, IgG4-related disease; IL-2, interleukin-2.