Table 3

Comparison of physician-diagnosed IIM subgroups with IIM subgroups defined according to the classification tree among patients meeting the EULAR/ACR classification criteria for IIM

Physician-diagnosed subgroupsClassification tree subgroups*Total
 JDMDMADMIBMPM
JDM2350000235
DM01916215214
ADM11300032
IBM00066571
PM0703131141
IMNM00001010
Total2361993671161703
% of all IIM33.628.35.110.122.9
% of adult IIM42.67.715.234.5
  • *Classification of IIM by the EULAR/ACR classification criteria for IIM, using a 55% probability cut-off for classification, followed by the classification tree for subclassification.

  • ACR, American College of Rheumatology; ADM, amyopathic dermatomyositis; DM, dermatomyositis; EULAR, European League Against Rheumatism; IBM, inclusion body myositis; IIM, idiopathic inflammatory myopathies; IMNM, immune-mediated necrotising myopathy; JDM, juvenile dermatomyositis; PM, polymyositis.