Case 1Case 2Case 3
Sex, ageMale, 59 yearsMale, 55 yearsMale, 50 years
Type of SScLimitedLimitedDiffuse
Disease duration at Tx6 years7 years4 years
ANANegative1/320, speckled, no SSc-specific antibodyNegative
Pre-Tx
NYHA classIVIIIIII
LVEF20%40%40%
RHC: mPAP in mmHg262031
RHC: PCWP in mmHg201428
Post-Tx
NYHA classIII
LVEF60%55%60%
RHC: mPAP in mmHg191321
RHC: PCWP in mmHg12812
  • Tx: Transplant; mPAP: Mean pulmonary artery pressure; PCWP: Pulmonary capillary wedge pressure.