Case 1 | Case 2 | Case 3 | |
---|---|---|---|
Sex, age | Male, 59 years | Male, 55 years | Male, 50 years |
Type of SSc | Limited | Limited | Diffuse |
Disease duration at Tx | 6 years | 7 years | 4 years |
ANA | Negative | 1/320, speckled, no SSc-specific antibody | Negative |
Pre-Tx | |||
NYHA class | IV | III | III |
LVEF | 20% | 40% | 40% |
RHC: mPAP in mmHg | 26 | 20 | 31 |
RHC: PCWP in mmHg | 20 | 14 | 28 |
Post-Tx | |||
NYHA class | I | I | I |
LVEF | 60% | 55% | 60% |
RHC: mPAP in mmHg | 19 | 13 | 21 |
RHC: PCWP in mmHg | 12 | 8 | 12 |
Tx: Transplant; mPAP: Mean pulmonary artery pressure; PCWP: Pulmonary capillary wedge pressure.