Table 1.

Clinical characteristics at presentation and initial treatment of IgAV

Male, %57.6
Median age (IQR), years65.4 (41.3–77.4)
Purpura, # (%)139 (100)
 necrotic, # (%)61 (43.9)
 generalized, # (%)63 (45.3)
Joint involvement, # (%)62 (44.6)
GI tract involvement, # (%)49 (35.3)
 severe GI, # (%)13 (9.4)
Renal involvement, # (%)69 (49.6)
 severe, # (%)19 (13.7)
Median BVAS-3 (IQR)10 (5–16)
Malignancy, # (%)3 (2.2%)
  • Legend: # – number of patients; IQR – interquartile range; GI – gastrointestinal tract; severe GI tract involvement- - bloody diarrhoea or ileus or surgical intervention; severe renal involvement – acute renal failure or nephrotic syndrome; BVAS-3 – Birmingham vasculitis activity score; Malignancy – concurrently diagnosed malignancy.