Table 1

Demographic characteristics of 136 cryopyrin-associated periodic syndrome (CAPS) patients

n%
Gender
 Male6950
 Female6750
 Gender ratio1
Origin
 Caucasian12894
 Asian86
Family history of CAPS
 Yes7655.8
 No5439.7
 Unknown63.6
Median (IQR 25–75)
Age at onset (years)0.8 (0.1–5)
Age at diagnosis (years)15 (5–36)
Age at last visit (years)15 (8–35)