Table 1

Summary of studies including the incidence of primary Sjogren’s syndrome

AuthorYearCountryStudy periodCases findingStudy designCase ascertainmentAge of patients with pSS*pSS cases (n)Person- yearsFemale/male (n)IR (95% CI)/100 000Quality
Pillemer et al312001USA (Minnesota)1976–1992Medical record searchPopulation basedNS59.0±15.8531 358 99451/26.90 (5.01 to 8.79)Good
Plesivcnik Novljan et al322004Slovenia (Ljubljana)2000–2002Medical record searchPopulation basedEC-1996†51.3±14.5711 799 68565/6‡7.22 (5.47 to 8.98)Good
Alamanos et al14§2006Greece (north-west Greece)1982–2003Medical record search, personal registry physiciansPopulation basedAECG-2002¶55.4±12.54227 962 264402/2010.10 (9.11 to 11.08)Good
Weng et al332011China (Taiwan)2005–2007NHI Research DatabasePopulation basedNS53.5±14.2335255 866 6663040/31211.00 (10.61 to 11.39)Good
Yu et al13§2013China (Taiwan)2000–2008NHI Research DatabasePopulation basedICD codes SystemNS8558 066 037736/11918.50 (17.16 to 19.84)Good
See et al19§2013China (Taiwan)2005–2009NHI Research DatabasePopulation basedICD codes systemNS5834 953 660501/8320.05 (18.29 to 21.80)Good
  • *Ages shown as mean±SD.

  • †EC-1996 is European classification criteria for Sjogren's syndrome published in 1996.

  • ‡Fifty per cent of the study population was assumed to be female.

  • §The study reported the prevalence and incidence rate of pSS.

  • ¶AECG-2002 is a revised version of the European criteria for Sjogren’s syndrome proposed by the American-European Consensus Group in 2002.

  • NS, no stated; pSS, primary Sjögren's syndrome.