Table 1

Overarching principles for CAPS, TRAPS and MKD

Overarching principles	L	S	Agree (%)
Management of patients with AID should ideally be guided by a multidisciplinary team in a tertiary centre with expertise in AID, with access to genetic counselling	4	D	100
The care of patients with AID should include shared patient-centred and family-centred decision-making with the multidisciplinary team	4	D	100
Aims of the treatment of AID include: Early and rapid control of disease activity Prevention of disease and treatment-related damage Enabling participation in daily activities Improvement of health-related quality of life	4	D	100
In patients with AID, psychosocial support is recommended as appropriate	4	D	100

L, level of evidence; 4, expert opinion; S, strength of recommendation; D, based on level 4 evidence.9 Agree, percentage of experts who agreed on the recommendation during the final voting round of the consensus meeting.
AID, autoinflammatory diseases; CAPS, cryopyrin-associated periodic syndromes; MKD, mevalonate kinase deficiency; TRAPS, tumour necrosis factor receptor-associated periodic syndrome.