Table 1

IgG4-Related Diseases (IgG4-RD) are a Family Immuno-proliferative Disorders

▸  Type 1 autoimmune pancreatitis or AIP (IgG4-related pancreatitis)
▸  IgG4-related sclerosing cholangitis
▸  Mikulicz's disease (IgG4-related dacryoadenitis and sialadenitis)
▸  Sclerosing sialadenitis (Küttner's tumor, IgG4-related submandibular gland disease)
▸  Inflammatory orbital pseudotumor (IgG4-related orbital inflammation or orbital inflammatory pseudotumor)
▸  Chronic sclerosing dacryoadenitis (lacrimal gland enlargement, IgG4-related dacryoadenitis)
▸  A subset of patients with “idiopathic” retroperitoneal fibrosis (Ormond's disease) and related disorders (IgG4-related retroperitoneal fibrosis, IgG4-related mesenteritis)
▸  Chronic sclerosing aortitis and periaortitis (IgG4-related aortitis or periaortitis)
▸  Riedel's thyroiditis (IgG4-related thyroid disease)
▸  IgG4-related interstitial pneumonitis and pulmonary inflammatory pseudotumors (IgG4-related lung disease)
▸  IgG4-related kidney disease (including tubulointerstitial nephritis and membranous glomerulonephritis secondary to IgG4-RD)
▸  IgG4-related hypophysitis
▸  IgG4-related pachymeningitis