▸ Type 1 autoimmune pancreatitis or AIP (IgG4-related pancreatitis) |
▸ IgG4-related sclerosing cholangitis |
▸ Mikulicz's disease (IgG4-related dacryoadenitis and sialadenitis) |
▸ Sclerosing sialadenitis (Küttner's tumor, IgG4-related submandibular gland disease) |
▸ Inflammatory orbital pseudotumor (IgG4-related orbital inflammation or orbital inflammatory pseudotumor) |
▸ Chronic sclerosing dacryoadenitis (lacrimal gland enlargement, IgG4-related dacryoadenitis) |
▸ A subset of patients with “idiopathic” retroperitoneal fibrosis (Ormond's disease) and related disorders (IgG4-related retroperitoneal fibrosis, IgG4-related mesenteritis) |
▸ Chronic sclerosing aortitis and periaortitis (IgG4-related aortitis or periaortitis) |
▸ Riedel's thyroiditis (IgG4-related thyroid disease) |
▸ IgG4-related interstitial pneumonitis and pulmonary inflammatory pseudotumors (IgG4-related lung disease) |
▸ IgG4-related kidney disease (including tubulointerstitial nephritis and membranous glomerulonephritis secondary to IgG4-RD) |
▸ IgG4-related hypophysitis |
▸ IgG4-related pachymeningitis |