Table 3

Accuracy measures of the AIDAI total score (0/1 scoring) for 98 patients with a hereditary recurrent fever syndromes diagnosis

Activity as defined by the AIDAI total scoreActivity as defined by consensusTotal
ActiveInactive
≥9 active64 (89%)2 (8%)66
<9 inactive8 (11%)24 (92%)32
Total722698
  • A total AIDAI score <9 separates inactive from active patients (total score ≥9).

  • AIDAI, Auto-Inflammatory Diseases Activity Index.