Case 1Case 2Case 3Case 4
SexFemaleFemaleFemaleFemale
Previous autoimmune diseaseRaynaud’s disease, Jaccoud’s arthropathyNoneAutoimmune thyroiditisNone
Diagnosis of Kikuchi-Fujimoto disease
 Year1990200220082010
 Age at KFD diagnosis40 years24 years13 years18 years
 Lymph-node siteAxillary, inguinalLaterocervicalSupraclavicularLaterocervical
 ANANegativePositivePositiveNegative
 Anti-DNANegativeNegativeNegativeNegative
 Concomitant autoimmune disesaseNoneIdiopathic Thrombo-cytopenic PurpuraNoneNone
 Diagnosis methodLymph-node biopsyLymph-node biopsyLymph-node biopsyLymph-node biopsy
 KFD recurrenceNoYesYesYes
Clinical course
 Autoimmunity findingsPleuropericarditis, lymphopeniaOral thrush, chilblain, lymphopenia
 Serological markersANA+, Anti-DNA+, Anti-phospholipid+ANA+, Anti-DNA+
Diagnosis of SLE
 Year19922006
 Age at the time of SLE diagnosis42 years28 years