Final core set of domains and tools defined by the Delphi survey
| Domains | Tools |
|---|---|
| Clinical | Dyspnoea (excluding other underlying causes of dyspnoea, not related to pulmonary hypertension): |
| Progressive dyspnoea over the past 3 months | |
| Unexplained dyspnoea | |
| Worsening of WHO dyspnoea functional class | |
| Right heart failure without apparent aetiology: | |
| Any finding on physical examination suggestive of elevated right heart pressures (jugular venous distension, accentuated P2, TR murmur) | |
| Any sign of right heart failure | |
| Echocardiography | sPAP >45 mm Hg |
| Dilation of right ventricle | |
| Pulmonary function tests | DLCO <50% without pulmonary fibrosis |
DLCO, diffusion lung capacity for carbon monoxide; sPAP, systolic pulmonary artery pressure; TR, tricuspid regurgitation.