Table 3

Dose by phenotype and weight groups

Weight groups
Phenotype (>40 kg/≤40 kg)>40 kg Mean
dose, mg
≤40 kg* Mean
dose, mg/kg
FCAS (27/3)188.92.7
MWS (90/13)199.85.5
NOMID/CINCA (19/13)228.95.8
  • Values are n (%).

  • * On average dosed on mg/kg basis.

  • CINCA, chronic infantile neurological cutaneous and articular syndrome; FCAS, familial cold autoinflammatory syndrome; MWS, Muckle–Wells syndrome; NOMID, neonatal-onset multisystem inflammatory disease.