Table 3

Causes of death within and after the first year of follow-up, respectively

<1 Year>1 YearTotal (%)
Cause of deathPrimary causeContributing factorPrimary causeContributing factorPrimary causeContributing factor
Active vasculitis11 (18.6)17 (28.8)6 (8.1)7 (9.5)17 (12.8)24 (18.0)
 Pulmonary haemorrhage628
Infection28 (47.5)31 (52.5)15 (20.3)23 (31.1)43 (32.3)54 (40.6)
 Pneumonia15823
 Sepsis8715
 CMV22
 PCP32
Cardiovascular9 (15.3)11 (18.6)19 (25.7)21 (28.4)28 (21.1)32 (24.1)
 Myocardial infarction246
 Cerebrovascular accident224
 Pulmonary embolus22
 Sudden death134
Malignancy0 (0)16 (21.6)18 (24.3)16 (12.0)18 (13.5)
 Solid organ1212
 Haematological44
Miscellaneous6 (10.2)9 (12.2)15 (11.3)
 Pulmonary fibrosis336
Unknown5 (8.5)9 (12.2)14 (10.5)
Total5974133
  • Primary cause: Number of patients where specific factor was main factor of death.

  • Contributing factor: All patients where specific cause contributed to death (including primary cause).

  • CMV, cytomegalovirus infection; PCP, Pneumocystis jiroveci pneumonia.