Table 1

κ Level of agreement (95% CI) between the consensus panel classification (columns) and the diagnosis of the treating physician (rows).

κ Agreement (95% CI)HSPc-PANc-WGc-TAc-Other or no consensusTotal
HSP0.96 (0.84 to 1.00)56460
c-PAN0.73 (0.62 to 0.84)3812160
c-WG0.88 (0.76 to 0.99)51960
c-TA0.84 (0.73 to 0.96)481260
c-Other0.53 (0.43 to 0.64)13940
Total0.79 (0.73 to 0.84)5638534885280
  • κ Statistics for agreements were computed separately for each of the c-vasculitis entities (treating physician vs consensus panel) and included also misclassified cases (c-other and no consensus); κ levels of 0.61–0.8 are substantial, >0.8 identifies an almost perfect agreement.26 27

  • c-PAN, childhood polyarteritis nodosa; c-TA, c-Takayasu arteritis; c-WG, c-Wegener granulomatosis; HSP, Henoch–Schönlein purpura.