Intravenous immunoglobulin | 2 g/kg over 5 days | Muso et al, Jayne et al
77 78
|
15-Deoxyspergualin | 0.5 mg/kg/day till white cell count nadir of 3000/μl, then wait until the white cell count returns to ⩾ 4000/μl and repeat the dose for six cycles | Burke et al
79
|
Anti-thymocyte globulin | 2.5 mg/kg/day for 10 days adjusted according to lymphocyte count: no anti-thymocyte globulin if <150/μl, 1.5 mg/kg/day if 150–300/μl, full dose if >300/μl | Schmitt et al
35
|
Infliximab | 3–5 mg/kg/infusion every 1 to 2 months | Booth et al
80
|
Mycophenolate mofetil | 2 g/day | Koukoulaki et al, Stassen et al
74 81
|
Rituximab | 375 mg/m2 body surface area weekly for 4 weeks | Keogh et al, Keogh et al, Stasi et al, Brihaye et al, Eriksson et al
82
–
86
|