Table 1 Characteristics of controls, patients with IPAH, SSc–nonPAH and SSc–PAH
Controls (n = 21)IPAH (n = 20)SSc–nonPAH (n = 19)SSc–PAH (n = 21)
PAH rest (n = 13)PAH exercise (n = 8)
Age, year (SD)37.7 (10.7)46.4 (12.0)56.0 (10.7)63.1 (15.6)62.7 (15.6)*
Female (%)21 (100)19 (86)18 (95)13 (100)7 (88)†
RP (%)01 (5)17 (90)13 (100)8 (100)‡
Duration of RP, year (95% CI)NA27 (NA)6.3 (4.0 to 11.9)15.3 (10.9 to 21.3)6.6 (2.7 to 16.3)§
Good/moderate image quality20/119/115/412/15/3†
  • IPAH, idiopathic pulmonary arterial hypertension; NA, not applicable; PAH, pulmonary arterial hypertension; RP, Raynaud’s phenomenon; SSC, systemic sclerosis; SSc–nonPAH, SSc without PAH; SSc–PAH, SSc with PAH.

  • *Differences significant (p<0.05) between categories.

  • †Differences not significant between categories.

  • ‡Difference not significant between SSc-non PAH and SSc–PAH.

  • §Difference significant (p<0.05) between SSc–PAH at rest and SSc-nonPAH; difference not significant between SSc–PAH at rest and SSc–PAH during exercise.