Demographics of the cohort
| Diagnosis | No | Gender M/F | Median age (lower quartile, upper quartile) | Median duration in months (lower quartile, upper quartile) | ANCA by indirect immunofluorescence† | |
| cANCA | pANCA | |||||
| Takayasu arteritis | 9 | 0/9 | 37 (32, 58.5) | 49 (30, 150) | ||
| Polyarteritis nodosa | 10 | 5/4* | 62 (30.5, 67) | 60.5 (45, 85.5) | ||
| Wegener’s granulomatosis | 155 | 82/72* | 58 (45, 68) | 55.5 (12, 113) | 45 | 4 |
| Churg–Strauss syndrome | 28 | 17/11 | 59 (48, 61) | 60 (12, 120) | 3 | 3 |
| Microscopic polyangiitis | 15 | 8/7 | 68 (58, 76) | 12 (3, 36) | 0 | 7 |
| Henoch–Schönlein purpura | 10 | 7/3 | 45 (34, 61) | 39 (19, 66) | ||
| Cryoglobulinaemic vasculitis | 6 | 1/5 | 69.5 (65, 82) | 9 (0, 132) | ||
| Cutaneous vasculitis | 11 | 3/8 | 45 (22, 67) | 48 (36, 78) | ||
| Behçet disease | 25 | 10/15 | 42 (35.5, 48) | 102 (40, 165) | ||
| Cerebral vasculitis | 9 | 3/6 | 56 (52.5, 62) | 1 (0, 27) | ||
| Rheumatoid vasculitis | 8 | 3/5 | 69.5 (65.5, 76) | 16.5 (4, 39) | ||
*Gender was not recorded for one patient; †of the 198 patients with ANCA-associated vasculitis (Wegener’s granulomatosis, microscopic polyangiitis and Churg–Strauss syndrome), 102 were tested for ANCA within 30 days of the Birmingham Vasculitis Activity Score assessment, 67 were positive; the ANCA pattern in five patients was not recorded. Seventeen patients had “other” vasculitis syndromes and data for IC patients were missing.
ANCA, antineutrophil cytoplasmic antibody; cANCA, cytoplasmic pattern; pANCA, perinuclear pattern.