Table 1 Patient characteristics at study entry
PatientAge/age at onset, yearsRace/sexPrior disease manifestationsPrior immunosuppressivesPrednisone dose, mg
00126/21A/FGN IV, pleurisy, arthritis, leucopoenia, alopecia, skin, anaemiaCYC, AZA, MMF10
00259/44C/FSkin, arthritis, alopeciaAZA5
00325/15C/FGN IV, anaemia, DAHCYC, pulse steroids10
00439/33A/FSkin, arthritis, leucopoenia, peritonitisAZA, CYC, pulse steroids, thalidomide60
00537/34AH/FLeucopoenia, skin, arthritisAZA, dapsone70
00635/22A/FSkin, mesenteric vasculitis, pleuro-pericarditis, arthritis, anaemia, leucopoeniaAZA, pulse steroids15
00731/22A/FSkin, arthritis, anaemia, pericarditis, DAH, GN-IIAZA, MTX15
00842/34C/FRash, cutaneous lupus lesions, discoid lesionsAZA30
00939/28C/MGN I/II, rash, anaemia, leucopoenia, arthritis, pericarditisAZA, CYC20
01039/19C/FNephritis, arthritis, rash, pleuritis, lymphopoeniaMMF20
01145/13C/FShrinking lung disease, pleurisy, pericarditis, nephritis, arthritis, lymphopoeniaCYC, MTX, MMF, AZA12
01246/29A/FNephritis, arthritis, leucopoeniaAZA10
01343/34A/FPleurisy, arthritis, proteinuria, lymphopoeniaAZA, MTX, CYC, MMF20
01456/51C/FArthritis, anaemia, rashAZA, MTX, MMF, adalimumab, etanercept, infliximab10
01541/33A/FPleuritis, arthritis, rash, alopecia, neuropathy, vasculitisLEF, MMF, MTX, CYC, AZA20
01649/28C/FRash, arthritis, pleuritis, proteinuriaMMF, AZA9
01737/23A/FArthritis, pleuritis, thrombocytopoenia, pericarditisAZA5
01856/50C/FPleuritis, pericarditis s/p window, haematuria, leucopoenia, anaemiaAZA20
01923/20C/FRash, arthritis, pleuritisAZA20
02024/17C/FNephritis, leucopoenia, anaemia, arthritis, ulcersPulse steroids5
02128/21C/FMalar rash, photosensitivity, oral ulcers, renal disorder, elevated ANA, anti-DNACYC, MMF15
02248/38A/FPericarditis, alopecia, pleuritis, arthritisMTX10
02323/14C/FFatigue, headaches, arthritis, rash, mucosal ulcersAZA10
02440/35A/MPericarditis, rash, alopecia, arthritis, xerostomiaAZA10
  • A, African–American; AH, African–American/Hispanic; ANA, antinuclear antibodies; AZA, azathioprine; C, Caucasian; CYC, cyclophosphamide; DAH, diffuse alveolar haemorrhage; F, female; GN, glomerulonephritis (following numeral indicates World Health Organization histological class); LEF, leflunomide; M, male; MMF, mycophenolate mofetil; MTX, methotrexate; s/p, status post.