Patient | Age/age at onset, years | Race/sex | Prior disease manifestations | Prior immunosuppressives | Prednisone dose, mg |
001 | 26/21 | A/F | GN IV, pleurisy, arthritis, leucopoenia, alopecia, skin, anaemia | CYC, AZA, MMF | 10 |
002 | 59/44 | C/F | Skin, arthritis, alopecia | AZA | 5 |
003 | 25/15 | C/F | GN IV, anaemia, DAH | CYC, pulse steroids | 10 |
004 | 39/33 | A/F | Skin, arthritis, leucopoenia, peritonitis | AZA, CYC, pulse steroids, thalidomide | 60 |
005 | 37/34 | AH/F | Leucopoenia, skin, arthritis | AZA, dapsone | 70 |
006 | 35/22 | A/F | Skin, mesenteric vasculitis, pleuro-pericarditis, arthritis, anaemia, leucopoenia | AZA, pulse steroids | 15 |
007 | 31/22 | A/F | Skin, arthritis, anaemia, pericarditis, DAH, GN-II | AZA, MTX | 15 |
008 | 42/34 | C/F | Rash, cutaneous lupus lesions, discoid lesions | AZA | 30 |
009 | 39/28 | C/M | GN I/II, rash, anaemia, leucopoenia, arthritis, pericarditis | AZA, CYC | 20 |
010 | 39/19 | C/F | Nephritis, arthritis, rash, pleuritis, lymphopoenia | MMF | 20 |
011 | 45/13 | C/F | Shrinking lung disease, pleurisy, pericarditis, nephritis, arthritis, lymphopoenia | CYC, MTX, MMF, AZA | 12 |
012 | 46/29 | A/F | Nephritis, arthritis, leucopoenia | AZA | 10 |
013 | 43/34 | A/F | Pleurisy, arthritis, proteinuria, lymphopoenia | AZA, MTX, CYC, MMF | 20 |
014 | 56/51 | C/F | Arthritis, anaemia, rash | AZA, MTX, MMF, adalimumab, etanercept, infliximab | 10 |
015 | 41/33 | A/F | Pleuritis, arthritis, rash, alopecia, neuropathy, vasculitis | LEF, MMF, MTX, CYC, AZA | 20 |
016 | 49/28 | C/F | Rash, arthritis, pleuritis, proteinuria | MMF, AZA | 9 |
017 | 37/23 | A/F | Arthritis, pleuritis, thrombocytopoenia, pericarditis | AZA | 5 |
018 | 56/50 | C/F | Pleuritis, pericarditis s/p window, haematuria, leucopoenia, anaemia | AZA | 20 |
019 | 23/20 | C/F | Rash, arthritis, pleuritis | AZA | 20 |
020 | 24/17 | C/F | Nephritis, leucopoenia, anaemia, arthritis, ulcers | Pulse steroids | 5 |
021 | 28/21 | C/F | Malar rash, photosensitivity, oral ulcers, renal disorder, elevated ANA, anti-DNA | CYC, MMF | 15 |
022 | 48/38 | A/F | Pericarditis, alopecia, pleuritis, arthritis | MTX | 10 |
023 | 23/14 | C/F | Fatigue, headaches, arthritis, rash, mucosal ulcers | AZA | 10 |
024 | 40/35 | A/M | Pericarditis, rash, alopecia, arthritis, xerostomia | AZA | 10 |
A, African–American; AH, African–American/Hispanic; ANA, antinuclear antibodies; AZA, azathioprine; C, Caucasian; CYC, cyclophosphamide; DAH, diffuse alveolar haemorrhage; F, female; GN, glomerulonephritis (following numeral indicates World Health Organization histological class); LEF, leflunomide; M, male; MMF, mycophenolate mofetil; MTX, methotrexate; s/p, status post.