Table 2 SRC-related clinical symptoms and laboratory findings in 50 SSc patients at the time of SRC
ParameterResults
Hypertension (blood pressure > 140 mmHg systolic and/or 90 mmHg diastolic), n (%)44 (88%)
Blood pressure mmHg (mean (SD))
    Systolic189.1 (39.9)
    Diastolic111.4 (23.6)
Cardiovascular signs
    Left ventricular failure, n (%)23 (46)
    Pericarditis, n (%)3 (6)
    Arrhythmia, n (%)9 (18)
Neurological signs, n (%)27 (54)
    Hypertensive encephalopathy, n (%)17 (34)
    Seizure, n (%)5 (10)
    Intracerebral haemorrhage, n (%)5 (10)
Oligoanuria, n (%) (n = 47)21 (44)*
Laboratory tests
    Mean white blood cell count/mm3 (mean (SD))10 561 (5813)
    Mean haemoglobin level, g/dl (mean (SD))9.4 (2.3)
    Mean platelet count/mm3 (mean (SD))149.04 (95.55)
    Thrombotic microangiopathy, n (%)23 (46)
    Mean serum creatinine level, μmol/l (mean (SD))468 (293) (median: 392)
    Mean creatinine clearance, ml/min (mean (SD))18.3 (15.3) (median: 14.3)
    Haematuria, n (%) (n = 31)*13 (42)
    Granular casts, n (%) (n = 30)*4 (13)
    Proteinuria, n (%) (n = 38)*20 (53)
  • *Values available for the number of patients indicated.

  • SRC, scleroderma renal crisis; SSc, systemic sclerosis; SD, standard deviation.