Table 4 Category of evidence, strength of recommendations and level of agreement of recommendations
Recommendation no.Category of evidenceStrength of recommendationLevel of agreement (VAS, mm)
Whole committeeExperts in the field
1 Eye involvementIbA/D9.57 (0.51)9.73 (0.47)
2 Refractory eye involvementIb/IIbC/D8.71 (0.91)8.9 (0.83)
3 Major vessel diseaseIIIC8.64 (1.01)8.88 (0.83)
4 AnticoagulationIVD8.50 (1.74)8.86 (1.46)
5 Gastrointestinal involvementIIIC8.71 (0.47)8.75 (0.46)
6 Joint involvementIbA9.0 (0.78)8.89 (0.78)
7 Neurological involvementIIIC/D8.50 (0.65)8.44 (0.73)
8 Ciclosporine A neurotoxicityIIIC8.79 (0.70)8.78 (0.68)
9 Mucocutaneous involvementIbA/C9.07 (0.47)9.11 (0.11)
  • Values are given as mean (SD) where appropriate.