Table 4

 Levels of tumour necrosis factor and tumour necrosis factor receptors 1 and 2 during crisis

TNF* (pg/ml)TNFR1† (ng/ml)TNFR2‡ (ng/ml)Mutation
NR, not reported; TNF, tumour necrosis factor; TNFR, tumour necrosis factor receptor.
*TNF during crisis (normal <13 pg/ml); †TNFR1 during crisis (normal 0.8–1.9 ng/ml); ‡TNFR2 during crisis (normal 2–6.6 mg/ml).
Patient 1401.1NRT50M/N
Patient 2290.4NRT50M/N
Patient 3330.6NRT50M/N
Patient 4270.71.8C30S/N
Patient 5241.2NRR92W
Patient 6400.94C30S/N
Patient 78.8499.6R92Q