Patients | 84 | 34 | — | 37 | 13 | — |
Sex | | | | | | |
M | 37 | 17 | >0.99 | 16 | 4 | >0.99 |
F | 47 | 17 | | 21 | 9 | |
Ethnicity | 56 C | 28 C | | 27 C | 1 C | |
| 16 MA | 3 MA | | 4 MA | 9 MA | <0.001 |
| 8 ME | 2 ME | >0.99 | 5 ME | 1 ME | |
| 2 NA | 1 NA | | 0 NA | 2 NA | |
| 1 I | 0 I | | 1 I | 0 I | |
Fever | 49 | 16 (48) | 0.128 | 26 (72) | 7 (46) | 0.30 |
Abdominal pain | 45 | 12 (38.7) | 0.028 | 24 (66) | 9 (70) | <0.99 |
Musculoskeletal involvement* | 44 | 15 (48) | 0.33 | 22 (61) | 7 (54) | 0.745 |
Cutaneous involvement† | 28 | 11 (35.5) | 0.99 | 13 (36) | 4 (35) | >0.99 |
Seritis‡ | 23 | 10 (32) | 0.59 | 9 (25) | 4 (35) | 0.96 |
Neurological involvement§ | 22 | 5 (16) | 0.39 | 10 (27.7) | 7 (54) | 0.172 |
Transit disorders¶ | 18 | 7 (22.6) | 0.99 | 8 (22.2) | 3 (35) | >0.99 |
Lymphadenopathy | 14 | 6 (19) | 0.13 | 2 (5) | 6 (46) | 0.003 |
Rhinolaryngeal involvement** | 9 | 4 (12) | 0.695 | 3 (8.3) | 2 (15.4) | 0.59 |
Amyloidosis | 8 | 2 (6.4) | 0.27 | 6 (16.6) | 0 (0) | 0.175 |
Periocular oedema | 8 | 4 (12) | 0.695 | 3 (8.3) | 1 (7.7) | >0.99 |
Ocular involvement†† | 5 | 2 (6.4) | 0.99 | 3 (8.3) | 0 (0) | 0.652 |
Mean age at the first episode (years) | 15.705 | 18.91 | 0.01 | 9.72 | 22.4 | 0.179 |
Mean duration of episodes (days) | 9.055 | 7.43 | 0.01 | 11.03 | 7.58 | 0.125 |
Frequency of episodes | | | | | | |
⩽1episode/month | 46 | 13 | 0.017 | 27 | 6 | 0.418 |
>1episode/month | 27 | 15 | | 8 | 4 | |
Not related | 11 | 6 | | 2 | 3 | |
Familial case of TRAPS | 36 | 7 (20.6) | <0.001 | 29 (78.4) | 0 (0) | <0.001 |
Sporadic case of TRAPS | 48 | 27 | | 8 | 13 | |