Table 1

 Patient profile

Patient NoDiagnosisSexAgePSmRSSMajor disorders associated with ADVC/TlcoAuto-antibodyPrior treatmentFollow up
(years)(%)(months)
PS, performance status; mRSS, modified Rodnan skin score for systemic sclerosis; AD, autoimmune disease; F, female; M, male; SSc, systemic sclerosis; IP, interstitial pneumonia; ADM, amyopathic dermatomyositis; WG, Wegener’s granulomatosis; PR3, proteinase 3; St, corticosteroids; CY, cyclophosphamide; CsA, ciclosporin A.
1SSc+SLEF54216IP, digital ulcer58/51Anti-Scl-70St, CY33
2SScM55215IP65/47Anti-Scl-70St25
3SScM58231IP63/44St22
4SScF54126IP73/60Anti-Scl-70St20
5SScF53128IP74/29Anti-Scl-70St17
6SScF48232IP77/25Anti-Scl-70St, CY, CsA13
7ADMF542IP50/50St, CY, CsA31
8WGM211ExophthalmosAnti-PR-3St, CY, CsA16