Table 6

 Classification criteria for Wegener’s granulomatosis

*Haematuria and/or significant proteinuria.
†If a kidney biopsy is done it characteristically shows necrotising pauci-immune glomerulonephritis.
ANCA, antineutrophil cytoplasmic antibodies.
Three of the following six features should be present:
• Abnormal urinalysis*
• Granulomatous inflammation on biopsy†
• Nasal sinus inflammation
• Subglottic, tracheal, or endobronchial stenosis
• Abnormal chest x ray or CT
• PR3 ANCA or C-ANCA staining