Table 2

 New classification of childhood vasculitis

I Predominantly large vessel vasculitis
• Takayasu arteritis
II Predominantly medium sized vessel vasculitis
• Childhood polyarteritis nodosa
• Cutaneous polyarteritis
• Kawasaki disease
III Predominantly small vessels vasculitis
(A) granulomatous
• Wegener’s granulomatosis
• Churg-Strauss syndrome
(B) non-granulomatous
• Microscopic polyangiitis
• Henoch-Schönlein purpura
• Isolated cutaneous leucocytoclastic vasculitis
• Hypocomplementic urticarial vasculitis
IV Other vasculitides
• Behçet disease
• Vasculitis secondary to infection (including hepatitis B associated polyarteritis nodosa), malignancies, and drugs, including hypersensitivity vasculitis
• Vasculitis associated with connective tissue diseases
• Isolated vasculitis of the central nervous system
• Cogan syndrome
• Unclassified