New classification of childhood vasculitis
| I Predominantly large vessel vasculitis |
| • Takayasu arteritis |
| II Predominantly medium sized vessel vasculitis |
| • Childhood polyarteritis nodosa |
| • Cutaneous polyarteritis |
| • Kawasaki disease |
| III Predominantly small vessels vasculitis |
| (A) granulomatous |
| • Wegener’s granulomatosis |
| • Churg-Strauss syndrome |
| (B) non-granulomatous |
| • Microscopic polyangiitis |
| • Henoch-Schönlein purpura |
| • Isolated cutaneous leucocytoclastic vasculitis |
| • Hypocomplementic urticarial vasculitis |
| IV Other vasculitides |
| • Behçet disease |
| • Vasculitis secondary to infection (including hepatitis B associated polyarteritis nodosa), malignancies, and drugs, including hypersensitivity vasculitis |
| • Vasculitis associated with connective tissue diseases |
| • Isolated vasculitis of the central nervous system |
| • Cogan syndrome |
| • Unclassified |