Treatment in the patients from the CAPS registry
| Treatment | n (%) |
|---|---|
| IVI, intravenous immunoglobulin. | |
| Anticoagulation | 173 (79) |
| Steroids | 158 (71) |
| Cyclophosphamide | 66 (30) |
| Plasma exchange | 60 (27) |
| IVI | 42 (19) |
| Dialysis | 30 (14) |
| Fibrinolysis | 8 (4) |
| Use of defibrotide | 4 (2) |
| Splenectomy | 3 (1) |
| Prostacyclin | 3 (1) |
| Leg amputation | 2 (1) |
| Other treatments | 9 (4) |