Table 3

Cumulative incidence at 30 year follow up of extra-articular disease manifestations

Extra-articular manifestationNumber of patients30 Year cumulative incidence (SE (%))
Pericarditis215.4 (2.6)
Pleuritis215.2 (2.4)
Felty’s syndrome91.6 (0.8)
Major cutaneous vasculitis193.6 (1.5)
Neuropathy112.2 (1.0)
Scleritis40.8 (0.6)
Episcleritis51.0 (0.4)
Retinal vasculitis00.0
Glomerulonephritis41.1 (1.5)
Other vasculitis10.2 (0.2)
Amyloidosis30.7 (0.9)
Keratoconjunctivitis sicca6111.6 (2.3)
Xerostomia40.7 (0.5)
Sjögren’s syndrome5811.4 (2.6)
Pulmonary fibrosis346.8 (1.9)
Bronchiolitis obliterans40.5 (0.8)
Cervical myelopathy122.4 (1.2)
Subcutaneous nodules17234.0 (3.4)
Other nodules00.0
Any24746.0 (3.4)
Malmö7816.7 (3.2)