Patients | Sex/age (years) | Neutropenia (×109/l)* | Associated cytopenia(s) | BM analysis | In vitro BM culture | T cell clone |
---|---|---|---|---|---|---|
F, female; BM, bone marrow; MMA, myeloid maturation arrest; N, normal; ND, not done; CFU-GM, colony forming unit-granulocyte monocyte; CFU-E, colony forming unit-erythroblast. | ||||||
*At diagnosis. | ||||||
1 | F/63 | 0.24 | – | MMA | N | – |
2 | F/30 | 0.25 | Thrombocytopenia | MMA CD4−, CD8− γδ T cell expansion | N | + |
3 | F/15 | 0.2 | – | N | ND | ND |
4 | F/74 | 0.5 | Thrombocytopenia | MMA | ↓ CFU-GM ↓ CFU-E | – |
5 | F/63 | 0.17 | Haemolytic anaemia Thrombocytopenia | N | ND | – |
6 | F/56 | 0.25 | – | Lymphocyte excess | N | – |
7 | F/42 | 0.34 | – | MMA | N | – |