Table 1

Haematological findings

PatientsSex/age (years)Neutropenia (×109/l)*Associated cytopenia(s)BM analysisIn vitro BM cultureT cell clone
F, female; BM, bone marrow; MMA, myeloid maturation arrest; N, normal; ND, not done; CFU-GM, colony forming unit-granulocyte monocyte; CFU-E, colony forming unit-erythroblast.
*At diagnosis.
1F/630.24MMAN
2F/300.25ThrombocytopeniaMMA
CD4−, CD8− γδ T cell expansion
N+
3F/150.2NNDND
4F/740.5ThrombocytopeniaMMA↓ CFU-GM
↓ CFU-E
5F/630.17Haemolytic anaemia
Thrombocytopenia
NND
6F/560.25Lymphocyte excessN
7F/420.34MMAN