Patient selection for determination of prevalence in a cohort of patients with SSc receiving regular follow up at our institution
| Category | No | Additional information |
|---|---|---|
| TLC, total lung capacity; NYHA, New York Heart Association; CTED, chronic thromboembolic disease. | ||
| Number receiving active follow up with serial investigations at study institution (excluding referrals) | 722 | 120 Men, 602 women |
| Echocardiography normal | 526 | 47 Fibrotics, 478 non-fibrotics |
| Patients with echo PASP >35 mm Hg | 132 | 13 Fibrotics, 119 non-fibrotics |
| Patients with normal PFTs | 435 | 615 PFTs available, 180 fibrotics, 84 non-fibrotics with PFT abnormal |
| Patients with Tlco<40% with no lung fibrosis on HRCT and/or TLC >70% | 24 | |
| Patients with Tlco fallen by 20% during past year with no lung fibrosis | 8 | |
| Patients with no dyspnoea | 542 | |
| Patients with explained cause of dyspnoea during study period | 156 | |
| Patients with unexplained dyspnoea by lung fibrosis echo | 18 | 11 NYHA II, 6 NYHA III |
| Patients potential candidates for catheterisation on above assessment | 164 | |
| Patients undergoing catheterisation | 147 | 12 Men, 135 women |
| Patients with PAH on catheterisation | 89 | 14 Men, 75 women; age 66 (7) years, |
| Findings in patients with no PAH on catheter | 58 | 36 No abnormality, 9 systolic and diastolic dysfunction, 10 diastolic dysfunction, 3 CTED |