Clinical data of patients with ATA and ACA
| Patient 1 | Patient 2 | Patient 3 | |
|---|---|---|---|
| *No data available. | |||
| Age at onset | 20 | 61 | 57 |
| Duration (years) | 18 | 10 | 10 |
| Raynaud's phenomenon | + | + | + |
| Puffy fingers/ hands | + (only initially) | + | + (recurrent) |
| Scleroderma | Hands, forearms, upper arms, face, trunk | Hands, forearms, upper arms, face, trunk | Hands, forearms, face |
| Fingertip necrosis | + (recurrent) | + (once) | + (recurrent) |
| Contractures | Fingers, toes, elbows | Fingers, elbows | Fingers |
| Calcinosis cutis | + | + | (+) |
| Telangiectasia | Generalised | Breast | − |
| Oesophageal hypomotility | + | ND* | + |
| Pulmonary fibrosis | − | + | − |
| Sicca symptoms | − | + | − |
| Renal disease | − | − | + (proteinuria, decreased GFR) |
| Arthralgia/arthritis | +/− | +/− | −/− |