No |
Norwich annual incidence/ million (95% CI) | No |
Lugo annual incidence/ million (95% CI) | |
Wegener's granulomatosis | 48 | 10.6 (7.8 to 14.0) | 11 | 4.9 (2.4 to 8.8) |
Male | 25 | 11.4 (7.4 to 16.8) | 4 | 3.6 (1.0 to 9.3) |
Female | 23 | 9.8 (6.2 to 14.7) | 7 | 6.1 (2.4 to 12.6) |
Churg-Strauss syndrome | 14 | 3.1 (1.7 to 5.2) | 2 | 0.9 (0.1 to 3.2) |
Male | 9 | 4.1 (1.9 to 7.7) | 1 | 0.9 (0.0 to 5.1) |
Female | 5 | 2.1 (0.7 to 5.0) | 1 | 0.9 (0.0 to 4.9) |
Microscopic polyangiitis | 38 | 8.4 (5.9 to 11.5) | 26 | 11.6 (7.6 to 17.0) |
Male | 25 | 11.4 (7.4 to 16.8) | 15 | 13.7 (7.6 to 22.5) |
Female | 13 | 5.5 (2.9 to 9.5) | 11 | 9.6 (4.8 to 17.2) |
Polyarteritis nodosa | 44 | 9.7 (7.0 to 13.0) | 14 | 6.2 (3.4 to 10.5) |
Male | 27 | 12.3 (8.1 to 17.8) | 7 | 6.4 (2.5 to 13.1) |
Female | 17 | 7.2 (4.2 to 11.6) | 7 | 6.1 (2.4 to 12.6) |
Total | 86 | 18.9 (15.1 to 23.4) | 41 | 18.3 (13.1 to 24.8) |
Male | 52 | 23.7 (17.6 to 34.1) | 21 | 19.1 (11.8 to 29.2) |
Female | 34 | 14.5 (10.1 to 20.2) | 20 | 17.4 (10.6 to 27.0) |
The ACR criteria were used for Wegener's granulomatosis, Churg-Strauss syndrome, and polyarteritis nodosa, the CHCC definition was used for microscopic polyangiitis.
The number of patients in each category is the number who fulfilled the criteria/definition. The total number of patients in each group was Norwich 86 and Lugo 41. Some patients fulfilled two sets of criteria–typically the ACR criteria for polyarteritis nodosa and the CHCC definition for microscopic polyangiitis. In Norwich 24 patients and in Lugo 12 patients fulfilled both the ACR criteria for polyarteritis nodosa and the CHCC definition for microscopic polyangiitis.