Cause of death in 17 patients with primary Sjögren's syndrome
| Cause of death | No of patients | Autopsy performed |
| Cardiovascular | 6 | 1 |
| Congestive heart failure | 5 | 1 |
| Myocardial infarction | 1 | — |
| Cerebrovascular | 3 | — |
| Cerebral infarction or haemorrhage | 3 | — |
| Malignancy | 4 | 2 |
| Malignant lymphoma | 2 | 2 |
| Sigmoid cancer | 1 | — |
| Rectal cancer | 1 | — |
| Infection | 3 | 1 |
| Pneumonia | 2 | — |
| Meningoencephalitis and osteomyelitis | 1 | 1 |
| Drug intoxication | 1 | 1 |
| Total | 17 | 5 |