Annual incidence of primary systemic vasculitis in three regions of Europe
| Criteria/ definition | Tromsø | Norwich | Lugo | ||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| n | /million (95% CI) | n | /million (95% CI) | n | /million (95% CI) | ||||||||
| WG1-150 | ACR1-151 | 43 | 10.5 (7.6 to 14.2) | 48 | 10.6 (7.8 to 14.0) | 11 | 4.9 (2.4 to 8.8) | ||||||
| CSS1-150 | ACR | 2 | 0.5 (0.06 to 1.8) | 14 | 3.1 (1.7 to 5.2) | 2 | 0.9 (0.1 to 3.2) | ||||||
| MPA1-150 | CHCC1-151 | 11 | 2.7 (1.3 to 4.8) | 38 | 8.4 (5.9 to 11.5) | 26 | 11.6 (7.6 to 17.0) | ||||||
| PAN1-150 | ACR | 18 | 4.4 (2.6 to 7.0) | 44 | 9.7 (7.0 to 13.0) | 14 | 6.2 (3.4 to 10.5) | ||||||
| PAN | CHCC | 2 | 0.5 (0.06 to 1.8) | 0 | 0.0 (0.0 to 0.8) | 2 | 0.9 (0.1 to 3.2) | ||||||
| Total | 56 | 13.7 (10.3 to 17.8) | 86 | 18.9 (15.1 to 23.4) | 41 | 18.3 (13.1 to 24.8) | |||||||
n = number of patients fulfilling each criteria in each centre, 18 Tromsø patients, 24 Norwich patients, and 12 Lugo patients fulfilled more than one set of classification criteria. Total represents the number of patients seen in each centre.
↵1-150 WG = Wegener's granulomatosis; CSS = Churg-Strauss syndrome; MPA = microscopic polyangiitis; PAN = polyarteritis nodosa.
↵1-151 ACR = American College of Rheumatology; CHCC = Chapel Hill Consensus definition.