Table 4

Findings in patients with Wegener's granulomatosis

Wegener's granulomatosis (n=27)
Patient number Age Sex Kidneys Skin Lungs ENT Other organs ANCA
Sym Sur Comment Biop Sym Biop Sym Sur Comment Biop Sym Sur Comment Biop Sym Sur Comment Biop
265M+protu.++++cough++bl.nas.dis.PR3
1165F+ery.++++fix.infil>1mo+++sinusit/mast.MPO
2120F++cyl.ery.protu.+++fix.infil>1mo++sinusit+PR3
2234M+ery.++++fix.infil>1mo++bl.nas.dis.PR3
2476F+protu.+++fix.infil>1moPR3
3341M+protu.+++fix.infil>1mo++sinusitPR3
3559M+ery.++++crusting+mononeur.PR3
3656M++otitisPR3
3746F+ery.+haemoptysis++sinusit+PR3
4575F+protu.+++fix.infil>1mo+pur.nas.dis.PR3
4968F+protu.++fix.infil>1mo+++sinusitPR3
6357F++fix.infil>1mo+++sinusitPR3
6963M++cyl.ery.protu.+++bl.nas.dis./crust+mult.infarctsPR3
7127F+++caverns>1moPR3
7528F++caverns>1mo++sinusit+PR3
7729M+protu.++++ac.h.lossPR3
8223F+++mastoiditisPR3
8431M++cyl.ery.protu.+++sinusitPR3
9376F++saddlenosePR3
9767M++fix.infil>1mo++pur.nas.dis.PR3
9862F+++sinusitsural nerve+PR3
9972F++++sinusit+PR3
10650M++++fix.infil>1mo++crusting+mononeur.PR3
12052F+protu.++++caverns>1mo++saddlenoseportio+PR3
12138M+protu.++++fix.infil>1mo++bl.nas.dis.PR3
12268F++caverns>1mo+PR3
12378F++++caverns>1mo+NEG
  • Sym: symptoms, Sur: surrogate, Biop: biopsy, PR3: proteinase -3, MPO: myeloperoxidase, NEG: negative, protu.: proteinuria, ery.: erythrocyturia, cyl.: cylindruria, fix. infil: fixed infiltrates, bl.nas.dis.: bloody nasal, discharge, sinusit: sinusitis, mast.: mastoiditis, pur.nas.dis.: purulent nasal discharge, crust: crusting, ac.h.loss: acute hearing loss, mononeur.: mononeuritis, mult.: multiple. Biop + indicates for kidneys: necrotising glomerulonephritis, skin: leucocytoclastic vasculitis, lungs: granulomatous inflammation, ENT: granulomatous inflammation, other organs: necrotising vasculitis.