Table 1

Main features of patients with Behçet’s disease complicated by endomyocardial fibrosis

Age, sex
ethnic origin
Signs of Behçet’s disease Vascular involvement Involved cavitary Cardiac failure Valvulopathy Diagnostic procedure
Case 134 yearsOral aphthaePhlebitisRight ventriclePresentTricuspidBiopsy
MaleGenital aphthae
AlgerianUveitis
Pseudofolliculitis
Skin hyperirritability
Case 232 yearsOral aphthaeStrokeLeft ventricleAbsentMitralSurgery
FemaleGenital aphthae
FrenchPseudofolliculitis
Skin hyperirritability
Arthritis
Case 324 yearsOral aphthaePhlebitis, arthritisRight ventriclePresentTricuspidSurgery
MaleGenital aphthae
TurkishPseudofolliculitis
Arthralgias
Case 427 yearsOral aphthaePhlebitisRight ventriclePresentTricuspidSurgery
MaleUveitis
AlgerianPseudofolliculitis
Skin nodules
Arthralgias
Case 545 yearsOral aphthaePhlebitisRight atrium and ventriclePresentTricuspidNecropsy
Bugeet al 5 MaleGenital aphthae
FrenchPseudofolliculitis
Skin nodules
Skin hyperirritability
Arthritis
Central nervous system involvement
Case 6NDNDNDNDNDNDNecropsy
Hamza2
Cases 7 and 8NDNDNDNDNDNDNecropsy
Lakhanpalet al 3 NDNDNDNDNDNDNecropsy
Case 930 yearsOral aphthaeRight ventriclePresentAbsentSurgery
El-Ramahiet al 6 MaleGenital aphthae
SaudiSkin nodules and pustules
Arthritis
Case 1035 yearsOral aphthaeLeft ventricleAbsentMitral and aorticBiopsy
Pena et al 7 MaleGenital aphthae
SpanishUveitis
Skin hyperirritability
Arthritis
  • ND=not determined.