Continuing Medical EducationPanniculitis. Part II. Mostly lobular panniculitis☆
Section snippets
Mostly lobular panniculitis with vasculitis (Table I)
With vasculitis Small vessels Venules Erythema nodosum leprosum Lucio's phenomenon Neutrophilic lobular (pustular) panniculitis associated with rheumatoid arthritis Large vessels Arteries Erythema induratum of Bazin Crohn's disease No vasculitis Few or no inflammatory cells Necrosis at the center of the lobule Sclerosing panniculitis With vascular calcification Calciphylaxis Oxalosis With needle-shaped crystals in adipocytes Sclerema neonatorum
Sclerosing panniculitis
Jorizzo et al,63 in 1991, proposed the term sclerosing panniculitis as the best name to describe a variant of panniculitis previously known by a variety of names, including hypodermitis sclerodermiformis,64 lipodermatosclerosis,65 and lipomembranous change in chronic panniculitis.66 The cutaneous lesions of this disorder consist of woodlike indurated plaques with erythema, edema, telangiectasia, and hyperpigmentation involving the lower legs with a stocking distribution. The condition is
Disorders erroneously considered as specific variants of panniculitis (Table II)
• Weber-Christian disease • Rothmann-Makai disease • Lipomembranous or membranocystic panniculitis • Eosinophilic panniculitis
Acknowledgements
Many colleagues contributed clinical photographs, histopathologic slides, or other material for this review. We are grateful to the following clinicians and pathologists: A. Bernard Ackerman, MD (United States); Adolfo Aliaga, MD (Spain); J. Andrew Carlson, MD (United States); Carlos Díaz, MD (Germany); Heinz Kutzner, MD (Germany); Arno Rutten, MD (Germany); Omar Sangueza, MD (United States); and H. Peter Soyer, MD (Austria). Catherine Sangueza read and corrected the manuscript.
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