Diffuse scleroderma6/11
Limited scleroderma5/11
Pulmonary hypertension4/11
History of digital ulcers5/11
Time of endurance in minutes (ergospirometry)5':32” (±65”)
Diffusion capacity (%pred)82±15
Pulmonary fibrosis7/11
VE/VCO2 (mean values ± sd)32±5
Patterns of capillaroscopy1/11 normal 1/11 early 4/11 active 5/11 late