| A | B | C | D | |
|---|---|---|---|---|
| Sex | Female | Male | Female | Male |
| Age at disease onset | 43 | 77 | 35 | 62 |
| Fever | Yes | No | No | No |
| Heliotrope rash | Yes | No | Yes | No |
| Gottron papules | Yes | No | No | No |
| Skin ulceration | No | No | No | Yes |
| Joint disease (J) | No | No | RA like | Palindromic like |
| Raynaud's disease | No | No | No | No |
| Muscular disease (M) | No | No | Yes | No |
| Pulmonary disease (P) | Bronchiolitis | Interstitial lung disease | No | Interstitial lung disease |
| Cardiac disease (Card) | No | Arrhythmias | Sinus tachycardia | No |
| Aldolase (N<7) | Normal | NA | 11 | 14,6 |
| ESR/CRP mg/dL | 30/4,5 | 41/13,7 | 102/8,1 | 50/1,8 |
| Ferritin (30–400 ng/ml) | 1253 | NA | 225 | 2437 |
| Electromyography | NA | NA | Normal | NA |
| Muscle biopsy | NA | NA | Miopathy | NA |
| Skin biopsy | DM | NA | Nonspecific | DM |
| Treatment | CC + CPM + TACR + IVIG | CC | CC + MTX + HCQ | CC + CPM + TACR |
| Outcome (months) | Death | Death | Clinical response (18 m) | Alive (16 m) |
RA = Rheumatoid Arthritis; NA = Not Avalaible; ANA = Antinuclear Antibodies; DM = Dermatomyositis; CC = Corticosteroids; CPM = Cyclophosphamide; TACR = Tacrolimus; IVIG = Intravenous Immunoglobulins; MTX = Methotrexate; HCQ = Hydroxychloroquine.