Table 1
PatientAge at HSCT (years)SexDisease duration at HSCT (years)BS manifestationsTreatment pre-HSCTHSCT IndicationFollow up (months)ComplicationsOutcomeTreatment post-HSCT
147M6OUTacrolimusMultiple Myeloma135NilOU GU (minor)Pred 4mg
GU
S
MSK
V
N
229M5OUMMFNeuro-Behçets80Nil1x flare 2013 (OU)AZA
GUTacrolimus
SIFX
OcularETN
NCYCP
ALN
351M4OUAZARefractory, severe OU & GU1DVTRemissionnil
GUMMF
SETN
VADA
NCertolizumab
Interferon
442FUnknownOUAZARefractory, severe OU & GU8Pneumonia & MucositisRemissionPred 40mg
GULeflunomide
SMTX
MSKThalidomide
GastroIFX
ADA
ETN
ALN
  • OU = oral ulceration, GU = genital ulceration, MSK = musculoskeletal, S = skin, N = neurological, V = vascular. AZA = azathioprine, CYCP = cyclophosphamide, MMF = mycophenolate motefil, MTX = methotrexate. ADA = adalimumab, IFX = Infliximab, ETN = Etanercept, ALN = Alentuzumab.