Table 1.

Distribution of clinical findings and organ involvement (n=52)

Constitutional symptoms, n (%)
 Fatigue31 (59.6)
 Tiredness16 (30.7)
 Night sweats15 (28.8)
 Weight loss14 (26.9)
 Fever13 (25)
Retroperitoneal fibrosis, n (%)23 (44.2)
Lymphadenopathy, n (%)20 (39.2)
Any cardiovascular involvement, n (%)15 (28.8)
 Periaortitis12 (23.1)
 Pericardium5 (9.6)
 Coronary periarteritis4 (7.7)
 Abdominal aort aneurysm1 (1.9)
Orbital pseudotumor, n (%)12 (23.1)
 Orbitalmass/proptosis6 (11.5)
 Extraoculary muscles6 (11.5)
Pancreas, n (%)12 (23.1)
Major salivary glands, n (%)11 (21.2)
Lacrimal glands, n (%)9 (17.3)
Mediastinal fibrosis, n (%)6 (11.5)
Ear, nose, sinuses, n (%)5 (9.6)
Lung fibrosis, n (%)5 (9.6)
Skin , n (%)4 (7.7)
Pleura, n (%)4 (7.7)
Gall bladder and Biliary ducts, n (%)4 (7.7)
Thyroid, n (%)3 (5.8)
Liver, n (%)3 (5.8)
Kidney (mass) , n (%)3 (5.8)
Pachymeningitis, n (%)2 (3.8)
  • Breast involvement: (n=1), tubulointerstitial nephritis (n=1).