Table 1

Patient	Sex	Diagnostic age	Onset age	Arthritis	Location	Other musculoskeletal manifestations	Extra-articular manifestations	MEFV Mutation	Homo/ Heterocytosis

1	M	47	40	Yes	Knee	No	No	p Glu148Gln	Heterocytosis
2	M	14	13	Yes	Knee	No	No	R202Q	Homocytosis
3	M	22	22	No		No	Lymphocytic myocarditis	p Glu148Gln	Heterocytosis
4	M	52	47	No		Arthralgias	Abdominal pain. Pleuritis	R202Q	Heterocytosis
5	M	39	20	Yes	PIPs	Arthralgias	Abdominal pain	R202Q	Heterocytosis
6	M	61	54	No		Tendinopathy	Recurrent pericarditis	R202Q	Homocytosis
7	M	17	16	No		No	Abdominal pain	R202Q	Heterocytosis