Table 1.

IgAV cases fulfilling EULAR/PRINTO/PRES but not ACR classification criteria

Patient (gender/age)Age <20 yrsPurpuraGIT inv.Renal inv.Joint inv.Skin biopsy; granulocytes in the vessel wallSkin biopsy; IgA depositionACR criteriaEULAR/PRINTO/PRES criteria
F/86NoYesNoNoNoNoYesNoYes
M/22NoYesNoYesNoNoYesNoYes
M/78NoYesNoYesNoNoYesNoYes
M/72NoYesNoNoNoNoYesNoYes
F/56NoYesNoNoNoNoYesNoYes
  • GIT, gastrointestinal; F, female; M, male; inv., involvement.