Attack featuresTNFRSF1A PSVTNFRSF1A R92Q VUS
Musculoskeletal pain82 (95%)29 (88%)
Fever76 (88%)31 (94%)
Abdominal pain71 (83%)22 (67%)
Constitutional upset63 (73%)25 (75%)
Rash55 (64%)13 (39%)
Eye involvement43 (50%)10 (33%)
Cervical Lymphadenopathy19 (22%)14 (42%)
Chest pain23 (27%)8 (24%)
Headache10 (12%)12 (36%)
Pharyngitis6 (7%)7 (21%)