| SoJIA Responders (N=10) | Total |
---|
| | Responders (N=18) | Non responders (N=17) |
---|
Age at onset (y) | 5, 5 (0.9-9) | 5, 6 (0-13) | 3, 4 (0.9-12) |
Time to start ANK (y) | 1.6, 2.6 (0.4-6) | 1.3, 2.8 (0.15-11) | 1.2, 3.4 (0.15-15) |
Follow-up time (y) | 5, 6 (2.5-9) | 5, 6 (1-16) | 4, 7 (0.7-16) |
Boys/Girls | 6 (60)/4 (40) | 11 (61)/7 (39) | 10 (59)/7 (41) |
Arthritis | 12, 11 (1-19) | 3, 6 (0-19) | 5, 8 (0-28) |
Rash | 10 (100) | 17 (95) | 13 (76) |
Serositis | 3 (30) | 6 (33) | 3 (18) |
Adenomegaly | 7 (70) | 9 (50) | 10 (59) |
MAS | 1 (10) | 3 (17) | 2 (12) |
ESR (mm/h) | 54, 66 (27-124) | 52, 56 (13-124) | 61, 53 (5-100) |
CRP (mg/l) | 55, 74 (9-158) | 52, 65 (0.8-158) | 25, 43 (0.2-138) |
Neutrophils (×103/μl) | 11.7, 14 (8.7-28) | 12.4, 15 (2.8-34) | 6.5, 7 (2.3-15) |
Genetic testing | 8 (80) | 16 (89) | 11 (65) |
Mutation | 3 (30) | 6 (33) | 8 (47) |
Asymptomatic | 10 (100) | 18 (100) | 12 (71) |