Table 1 Patient characteristics
ParameterValue
Patients with PAH10
Age, years56.4 (31–79)
Disease duration, years10.2 (2–24)
FVC/DLCO ratio1.6 (1.37–2.13)
ANA (n)10
SCL70 (n)2
ACA (n)2
  • Values are mean (range).

  • ACA, anticentromere antibodies; ANA, antinuclear antibodies; DLCO, CO diffusion; FVC, forced vital capacity; PAH, pulmonary arterial hypertension.