Table 3

 Central nervous system involvement in primary SS: clinical features recently described

Multiple sclerosis-like disease33,35,36
Myelopathy
    Acute myelitis37,38
    Chronic myelopathy39
Central pontine myelinolysis40
Parkinsonism41
Painful tonic/dystonic spasms42
Bell’s palsy43
Optic neuritis44
CNS vasculitis45
CNS T cell lymphoma46
Cerebral amyloid angiopathy47